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Oleh : Wilma Pratiwi030.05.234

Fakultas KedokteranUniversitas Trisakti

Pemimin! :dr. "hristo#el. P$ %&.O'

THALASEMIA PADA

KEHAMILAN

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P()*+,U-U+)

Yunani

(talassa) laut.

Pertama kalidikenal di

sekitar LautTengah

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anakanak!

Anemia ! "em#esaranlim"a

setelah #erusia $tahun

*okter di

*etroit U%+Tahun /25

ANEMIA

%&&LEY

*r. enton"oole

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(P*(O-O'T,+-+%(+

$''.''' #aidilahirkan denganthalasemia "arah

tia" tahun di dunia

(Arthur Schoenstadt,

2008)

(Arthur Schoenstadt,

2008)

(Arthur Schoenstadt,

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%+UK T,+-+%(+(Arthur Schoenstadt, 2008)

Sering ditemukan di daerah Timur Tengah* Italia* Yunani*

dan Asia Selatan* Asia

Daerah endemis malaria

(iklim tr,"is)

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(P*(O-O'T,+-+%(+

Thalasemia-Kulithitam./0mem#a1aminimal

satugen

Thalasemia2AsiatenggaradanMediterania

$dari3',rang%inaadalah4arrierthalasemia

(Diana Curran,2010)

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EPIDEMI&L&5I DIIND&NESIA

6 7 $' dari $'' ,rang mem#a1a genthalasemia

Menurut Yaasan ThalasemiaInd,nesia ang #er,#at di Pusat

Thalasemia 8S%M hingga 9uli '':(Nusrat Madina,

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%)T(%% ,(O'-O)

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TIN5KATIN S8I& 5&?E8 $ @

5&?E8 -

HEM&5L&>INP&8TLAND

@B

CET

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*(F)% T,+-+%(+

(Cunningham dkk,

2010)

(Cunningham dkk,

2010)

(Cunningham dkk,

2010)

(Cunningham dkk,

2010)

*Cunningham dkk,

2010

Kelainan darah ang diturunkan se4ara genetikautosomal resesi#) dimana ter9adi ke4a4atandalam "r,duksi rantai gl,#in ("r,tein dalam sel

darah merah)

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T,+-+%(+

*cunningham dkk, 2010

SINTESISA>N&8MAL

E8IT8&P&ESIS TIDAK

ECEKTIC

HEM&LISIS

ANEMI

A

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enurut'ehlah danor!enstern/667$ insidensithalasemia &adakehamilandalam era!airas di&erkirakanterda&at dalam

dari 300 8 500wanita hamil

(Cunningham dkk, 2010)

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)*9*U )O+-

; 5EN

5L&>IN-

K8&M&S&M N&.$6

DIN

2

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M

(Sylvieonglois dkk, 2008)

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Thalasem

ia -

Thalasemia 2

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K-+%FK+%T,+-+%(+

8ANTAI5L&>IN

-THALASEMIA

2THALASEMIA

$. THALASEMIA -

MAY&8. H#H DISEASE3. THALASEMIA - MIN&8;. SILENT %A8IE8

$. THALASEMIA 2

MAY&8. THALASEMIA 2MIN&8

(Cunningham dkk, 2010)

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