Atresia Duodeni Ppt
Transcript of Atresia Duodeni Ppt
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ATRESIA DUODENI
Disusun Oleh: -----------------------
Pembimbing: ------------------------
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DEFINISIAtresia duodeni adalah Suatu kondisi
dimanaduodenum tidak berkembang dengan
baik,sehingga tidak berupa saluran terbuka
darilambung yang tidak memungkinkanperjalanan makanan dari lambung ke
usus.
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EPIDEMIOLOGI
Insiden atresia duodenum di Amerika Serikat
adalah 1 per 6000 kelahiran. Obstruksiduodenum kongenital intrinsik
merupakan2/3 dari keseluruhan obstruksi duodenalkongenital (atresia duodenal 40-60%).
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ETIOLOGI
Kelainan bawaan yang penyebabnya belum diketahui secara jelas
Kelainan pengembangan embrionik saat masih dalam kehamilan.
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PATOFISIOLOGIGangguan perkembangan duodenum
terjadi akibat proliferasi endodermal yang tidak adekuat (elongasi saluran cerna melebihi proliferasinya) atau kegagalan rekanalisasi pita padat epithelial (kegagalan proses vakuolisasi).
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Tanda dan Gejala
Pembengkakan abdomen Pada bagian atasMuntah terus-menerus, meskipun bayi
dipuasakan selama beberapa jamTidak memproduksi urine setelah
beberapa kali buang air kecilMuntah banyak segera setelah lahir &
berwarna hijau karena empeduHilangnya bising usus setelah beberapa
kali buang air besar
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PEMERIKSAAN DIAGNOSTIK
1. Pemeriksaaan FisikInspeksi : tampak contour/
peristalsis lambung atau usus di daerah epigastrium
Palpasi : tampak distended pada daerah epigastrium disebabkan oleh duodenum dan gaster yang berdilatasi
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PEMERIKSAAN DIAGNOSTIK2. RadiografiThe Double Bubble Sign
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Supine frontal radiograph of the abdomen demonstrates the double bubble sign: an enlarged stomach (S) and proximal duodenum (D) in a neonate with duodenal atresia. Note the absence of distal gas.
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PEMERIKSAAN DIAGNOSTIK2. USGThe Double Bubble SignDijumpai Polihidramnion
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Sonography of the fetal abdomen (see pictures above), show 2 anechoic lesions (double bubble sign). The first bubble is formed by the fluid filled fetal stomach, the second being formed by the distended fetal duodenum. The obstruction is likely to be at the 2nd part of the duodenum. These ultrasound images (double bubble sign) suggest the likelihood of duodenal atresia.
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Prenatal sonogram in a sagittal oblique plane to the fetus demonstrates the double bubble sign in a fetus with duodenal atresia. In utero, the stomach (S) and duodenum (D) are filled with fluid.
Axial ultrasound, shows polyhydramnios and the stomach and duodenal bulb
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PEMERIKSAAN DIAGNOSTIK3. CT Scan
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PEMERIKSAAN DIAGNOSTIK4. MRI
Pictured (right) is a MRI of a fetus with duodenal atresia. The "double bubble" sign is indicated with arrows. Increased amniotic fluid also is seen, and it is consistent with polyhydramnios and intestinal obstruction.
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Duodenal atresia in a 35-week-old fetus. Coronal single-shot fast spin-echo MR image shows dilatation of the stomach (top arrow) and the proximal portion of the duodenum (bottom arrow), producing a “double bubble” appearance
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PENATALAKSANAAN
Pemasangan tuba orogastrikMemberikan cairan elektrolit
intravenaMengatasi sindrom downPembedahan
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KOMPLIKASI
Mudah terjadi dehidrasiTerjadi komplikasi lanjut setelah
pembedahan.
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PROGNOSA
Morbiditas dan mortalitas telah membaik secara bermakna selama 50 tahun terakhir.
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TERIMA KASIH