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IPERTENSI
IPERTENSI
PULMONALULMONAL
Prof.DR.dr.ZAINAL MUSTHAFA,MSi.,FS.,SpJP,FIHAProf.DR.dr.ZAINAL MUSTHAFA,MSi.,FS.,SpJP,FIHA
Dep. Kardiologi RSPAD-GSDep. Kardiologi RSPAD-GS
FK-UPN !e"era#$ Ja%ar"aFK-UPN !e"era#$ Ja%ar"a
7/25/2019 Hipertensi Pulmonal Upn 2015
2/20
PA
PA
Re&i&"e#&i A. P'l(o#ali&Re&i&"e#&i A. P'l(o#ali&
Gagal Ja#"'#g Ka#a#Gagal Ja#"'#g Ka#a#
Ke(a"ia# (e#dada%Ke(a"ia# (e#dada%
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3/20
Proses Selulerroses Seluler
PA
PA
Di&f'#g&i )#do"*elDi&f'#g&i )#do"*el
Ke&ei(+a#ga# +ioa%"if al Ke&ei(+a#ga# +ioa%"if al Ni"ro'& ide /N0Ni"ro'& ide /N0
Pro&"a&i%li#Pro&"a&i%li#
T*ro(+oa# AT*ro(+oa# A11 )#do"*eli'( 2 3)#do"*eli'( 2 3
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GANGGUAN
ANGGUAN
F'#g&i %a#al K 4 NaF'#g&i %a#al K 4 Na
)pre&i "ra#&por &ero"o#i#)pre&i "ra#&por &ero"o#i#
Prod'%&i (a"ri (e#i#g%a" /T'#i%a.ad!0Prod'%&i (a"ri (e#i#g%a" /T'#i%a.ad!0
7/25/2019 Hipertensi Pulmonal Upn 2015
5/20
KLASIFIKASI PALASIFIKASI PA
3.3. Idiopa"i%Idiopa"i%
1.1. Fa(ilialFa(ilial
5.5. 6er*'+'#ga# de#ga#6er*'+'#ga# de#ga# Pe#7a%i" Jari#ga#Pe#7a%i" Jari#ga#
PJ6PJ6
Hiper"e#&i Por"alHiper"e#&i Por"al Pe#gar'* o+a" 4 Toi#Pe#gar'* o+a" 4 Toi#
Lai#-lai#Lai#-lai#
7/25/2019 Hipertensi Pulmonal Upn 2015
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KLASIFIKASI PA -------2
LASIFIKASI PA -------2
8.8. HPA a%i+a" pe#7a%i" Ja#"'#g KiriHPA a%i+a" pe#7a%i" Ja#"'#g Kiri Ga#gg'a# f'#g&i A"ri'( 4 !e#"ri%el %iriGa#gg'a# f'#g&i A"ri'( 4 !e#"ri%el %iri
Ga#gg'a# %a"'p 9a#"'#g %iriGa#gg'a# %a"'p 9a#"'#g %iri
:.:. HPA a%i+a" pe#7a%i" Par' 4 Hipo%&iaHPA a%i+a" pe#7a%i" Par' 4 Hipo%&ia PPMPPM
Pe#7a%i" par' i#"re&"i"ialPe#7a%i" par' i#"re&"i"ial
Ga#gg'a# "id'rGa#gg'a# "id'r Hipo!e#"ila&i al!eoliHipo!e#"ila&i al!eoli
Ke"i#ggia#Ke"i#ggia#
Kelai#a# per"'(+'*a#Kelai#a# per"'(+'*a#
7/25/2019 Hipertensi Pulmonal Upn 2015
7/20
KLASIFIKASI PA -------3
LASIFIKASI PA -------3
;. HPA a%i+a" "*ro(+o e(+oli;. HPA a%i+a" "*ro(+o e(+oli
)(+oli p'l(o#al)(+oli p'l(o#al
)(+oli #o# "*ro(+o& /"'(or,para&i",+e#da)(+oli #o# "*ro(+o& /"'(or,para&i",+e#da
a&i#g0a&i#g0
7/25/2019 Hipertensi Pulmonal Upn 2015
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PATOGENESIS PA
ATOGENESIS PA
M'l"ifa%"orial, a.l. M'l"ifa%"orial, a.l.
!a&o %o#"ra%&i!a&o %o#"ra%&i
re(odelli#gre(odelli#g
o+&"r'%&i pe(+'l'* dara*o+&"r'%&i pe(+'l'* dara*
i#fla(a&i da# "*ro(+o&i&i#fla(a&i da# "*ro(+o&i&
7/25/2019 Hipertensi Pulmonal Upn 2015
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7/25/2019 Hipertensi Pulmonal Upn 2015
10/20
CURIGAURIGA
K)LUHAN 4 GANGGUANK)LUHAN 4 GANGGUAN
&e&a% "a#pa %elai#a# 7a#g lai#&e&a% "a#pa %elai#a# 7a#g lai#
>epa" lela*>epa" lela*
le(a*le(a*
a#gi#aa#gi#a&7#>ope&7#>ope
di&"e#&i a+do(e#di&"e#&i a+do(e#
7/25/2019 Hipertensi Pulmonal Upn 2015
11/20
DETEKSI PAETEKSI PA
)KG)KG
Fo"o T*oraFo"o T*ora
)%*o%ardiograp*7)%*o%ardiograp*7
A#giograp*7A#giograp*7
7/25/2019 Hipertensi Pulmonal Upn 2015
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KLASIFIKASI KLINISLASIFIKASI KLINIS
Te&" f'#g&i par'Te&" f'#g&i par'AGDAGD
=T=T
A#giograp*7A#giograp*7
7/25/2019 Hipertensi Pulmonal Upn 2015
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PENETUAN TYPEENETUAN TYPE
LA6. DARAH 4 IMUNLGILA6. DARAH 4 IMUNLGI
USG A6DM)NUSG A6DM)N
TR)ADMILL T)STR)ADMILL T)S
AGIGRAPH?AGIGRAPH?6IPS?6IPS?
7/25/2019 Hipertensi Pulmonal Upn 2015
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Dx PA
x PA
Die!"##"$ie!"##"$( PAP @ 5 ((Hg( PAP @ 5 ((Hg
PBPPBP 15 mmHg 15 mmHg
PWR > 3PWR > 3
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TATALAKSANA
ATALAKSANA
UMUMUMUM
+a"a&i a%"ifi"a&+a"a&i a%"ifi"a&
*i#dari %e"i#ggia#*i#dari %e"i#ggia#
>ega* i#fla&i>ega* i#fla&i
>ega* a#e(ia 4 H+>ega* a#e(ia 4 H+o+a"-o+a"a# 4o+a"-o+a"a# 4
7/25/2019 Hipertensi Pulmonal Upn 2015
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O%AT
%AT
ANTI KAGULANANTI KAGULAN
DIUR)TIKDIUR)TIK
KSIG)NASIKSIG)NASI
INTRPIKINTRPIK
==6 4 CASDILATASI==6 4 CASDILATASICAS DILATASICAS DILATASI
DLLDLL
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INTER&ENSI
NTER&ENSI
6ALN6ALN
TRANSPLANTASITRANSPLANTASI
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